What is a multilocular cystic Nephroma?
Multilocular cystic nephroma (MLCN) is a benign mixed mesenchymal and epithelial neoplasm of the kidney [1]. MLCN is classically described as a benign slow-growing renal tumor, and there are more than 200 cases reported in the literature.
Is Wilms tumor common?
Wilms’ tumor is the most common type of kidney cancer in children. Wilms’ tumor is a rare kidney cancer that primarily affects children. Also known as nephroblastoma, it’s the most common cancer of the kidneys in children. Wilms’ tumor most often affects children ages 3 to 4 and becomes much less common after age 5.
What is Nephroblastomatosis?
Nephroblastomatosis is a rare preneoplastic lesion defined as the presence of diffuse or multifocal nephrogenic rests. They are divided into 4 categories: perilobar, intralobar, combined, and universal. The aim of this report is to describe a case of diffuse hyperplastic perilobar nephroblastomatosis.
How rare is cystic nephroma?
Multilocular cystic nephroma is a rare entity of benign multicystic renal tumor. It was first described in 1892, and only approximately 200 cases have so far been reported in the related literature. The diagnosis is made based exclusively on the pathological finding.
What is a multilocular cyst?
1. a cyst containing several loculi or spaces. 2. a hydatid cyst with many small irregular cavities that may contain scoleces but generally little fluid.
What kind of surgery is needed for cystic nephroma?
Multilocular cystic renal tumors generally have the appearance of a multilocular cystic encapsulated mass on most modalities. May present as a large abdominal mass displacing and effacing adjacent bowel loops. Radical or partial nephrectomy is usually done, with lymph node excision.
Can a nephroma tumor be treated with radiation?
Since doctors often see good results with surgery and chemo, radiation is usually only used to treat certain types of nephromas, such as aggressive or late-stage Wilms tumors. Radiation treatments are usually short (30 minutes or less) and painless, but side effects such as fatigue, skin damage and nausea can occur.
When does cystic nephroma occur in middle age?
Classically, cystic nephromas were thought to occur in a bimodal age distribution, affecting young children and adults in middle age. The generic term “multilocular cystic renal tumor” was sometimes used for either cystic nephroma or cystic partially differentiated nephroblastoma, as they were indistinguishable except by microscopic analysis.
What kind of Nephroma is in the kidney?
What is nephroma? Nephroma is a tumor of the kidney cortex. The renal cortex is the outer portion of the kidney that filters the blood and removes waste inside the body. There are several kinds of nephroma, which fit into two main types: non-cancerous (benign) and cancerous (malignant). Non-cancerous forms of nephroma include: