What is pentalogy of Cantrell?
Pentalogy of Cantrell is a condition characterized by a combination of midline birth defects that can potentially involve the breastbone (sternum); the muscle that separates the chest cavity from the abdomen and aids in breathing (diaphragm); the thin membrane that lines the heart (pericardium); the abdominal wall; and …
What is ectopic cordis?
Ectopia cordis is a rare condition where a baby’s heart is located either partially or totally outside the chest. Only 8 out of 1 million babies are born with ectopia cordis, and 90% of these babies are either stillborn or die within the first 3 days of life.
How rare is Pentalogy of Cantrell?
The exact prevalence is unknown, but estimated to be 5.5 in 1 million live births. The symptoms of pentalogy of Cantrell are present at birth (congenital).
What is the meaning of Pentalogy?
A pentalogy (from Greek πεντα- penta-, “five” and -λογία -logia, “discourse”) is a compound literary or narrative work that is explicitly divided into five parts.
How is ectopia cordis treated?
To treat ectopia cordis itself, the main goal of surgery is to close the open chest wall. The surgeon and health care team will also place the heart within the thorax and repair any other cardiac defects. Whether or not these surgeries can happen depends on the kind of ectopia cordis.
Is Pentalogy of Cantrell fatal?
Surgical intervention for cardiac, diaphragmatic and other associated defects is necessary. Affected infants will require complex medical care and may require surgical intervention. In most cases, pentalogy of Cantrell is fatal without surgical intervention.
Is pentalogy a word?
noun. A combination of five mutually connected parts; a pentad.
What are the symptoms of ectopia cordis?
Ectopia cordis is defined by its main symptom: the heart being outside the body. Babies who have this condition often also have other “midline defects” (problems along the line going up and down in the center of the body, from the head to the groin), including: Cranial cleft (a split in the baby’s face shape)
What do you need to know about pentalogy of Cantrell?
Summary Summary. Pentalogy of Cantrell is a condition characterized by a combination of midline birth defects that can potentially involve the breastbone (sternum); the muscle that separates the chest cavity from the abdomen and aids in breathing (diaphragm); the thin membrane that lines the heart (pericardium); the abdominal wall; and the heart.
Is the pentalogy of Cantrell a congenital disorder?
General Discussion. Pentalogy of Cantrell is a rare disorder that is present at birth (congenital). Pentalogy of Cantrell is characterized by a combination of birth defects.
What is the name of the abdominal anomalies in Cantrell?
Pentalogy of Cantrell. Pentalogy of Cantrell is an unusual form of abdominal wall defect that consists of five (penta in ancient Greek) associated anomalies.
How is ectopia cordis related to Pentalogy of Cantrell?
Ectopia cordis is frequently, but not always associated with pentalogy of Cantrell. Omphalocele is an abdominal wall defect in which part of an infant’s intestines and abdominal organs protrude or stick out through the bellybutton. The intestines and organs are covered by a thin membrane or sac.