What is the surgical management of Hirschsprung disease?

What is the surgical management of Hirschsprung disease?

For most people, Hirschsprung’s disease is treated with surgery to bypass or remove the part of the colon that’s lacking nerve cells. There are two ways this can be done: a pull-through surgery or an ostomy surgery.

What is Abdominoperineal pull-through?

Purpose: Posterior sagittal abdominoperineal pull-through (PSAPP) was applied for the surgical treatment of Hirschsprung’s disease (HD) to decrease the incidence or eliminate the complications related to the major pullthrough procedures.

What is another name for Hirschsprung disease?

Hirschsprung’s disease is a rare congenital disorder that causes an obstruction (or blockage) of the intestine. This prevents normal bowel movements. You might hear doctors refer to this condition with other names, such as: Congenital megacolon or megarectum.

What is the possible complication of Hirschsprung disease after surgery?

Most people who undergo surgery for Hirschsprung’s disease recover without problems. Any time a person has a general anesthesia and surgery, however, there is a possibility of complications. These include bleeding, infection or a blockage of the bowel after surgery due to scarring or other factors.

Can Hirschsprung disease come back after surgery?

What is Swenson pull through procedure for Hirschsprung disease?

Swenson Pull-Through Procedure Marleta Reynolds Step 1: Surgical Anatomy ♦ Hirschsprung disease is the clinical manifestation of the absence of ganglion cells of the involved intestine. Ganglion cells are absent from the submucosal (Meissner) plexus as well as the intramuscular (Auerbach) plexus.

What is the Swenson procedure for surgical treatment of?

What is the Swenson procedure for surgical treatment of Hirschsprung disease? Author: Justin P Wagner, MD; Chief Editor: BS Anand, MD more… The Swenson procedure was the original pull-through procedure used to treat Hirschsprung disease.

What are the early signs of Hirschsprung disease?

The newborn has signs of bowel obstruction, including failure to pass meconium in the first 48 hours of life, abdominal distention, and vomiting. In infancy and childhood, symptoms of chronic constipation with or without episodes of explosive diarrhea can be present.

How many people have total colon Hirschsprung disease?

Total colon Hirschsprung disease occurs in between 3% and 10% of patients, with extension into the small bowel in less than 3% of patients. ♦ Trisomy 21, trisomy 18, Ondine curse, and a variety of other cristopathologic disorders are associated with Hirschsprung disease.

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