What is cystic hygroma with Septations?

What is cystic hygroma with Septations?

Cystic hygroma refers to the thickening of skin along the entire length of the fetal back as well as the visible division, or septations, between the skin and tissue. Septated cystic hygroma occurs early in pregnancy and is diagnosed in the first trimester.

Can a baby survive with cystic hygroma?

The overall survival rate for fetal cystic hygroma is 10%. Prognosis remains guarded regardless of all other factors until the fetus reaches 26 weeks’ gestation, after which time a 67% chance of ultimate survival can be expected.

How does cystic hygroma affect the baby?

A cystic hygroma can affect the amount of fluid surrounding your baby as well as within his or her body. When there is not enough or too much amniotic fluid, your baby has less of a chance for a healthy outcome. Too much fluid within the baby’s body (“hydrops”) occurs in 25 to 75 percent of cases.

What is a cystic hygroma in fetus?

Fetal cystic hygromas are congenital malformations of the lymphatic system appearing as single or multiloculated fluid-filled cavities, most often about the neck. They are thought to arise from failure of the lymphatic system to communicate with the venous system in the neck.

What syndrome is cystic hygroma commonly associated with?

Benign Neoplasms of the Neck Cystic hygroma may also be detected in utero by ultrasonography. Cystic hygroma is commonly associated with fetal hydrops and Turner syndrome.

Is cystic hygroma curable?

A cystic hygroma is usually treatable if it’s present at birth or develops later. The first step of treatment is surgery. The entire growth must be removed to prevent it from coming back. In some cases, however, your doctor may not want to remove large cystic hygromas.

Is cystic hygroma a genetic disorder?

A cystic hygroma may be caused by genetic or environmental factors that cause abnormal development of the lymphatic vascular system during embryonic growth. It may occur on its own or as part of a genetic syndrome with other features, such as Turner syndrome, Down syndrome or Noonan syndrome.

How common is fetal cystic hygroma?

According to The Fetal Medicine Foundation, cystic hygromas affect 1 in 800 pregnancies and 1 in 8,000 live births. In 80 percent of cases, cystic hygromas appear on the face, including the head, neck, mouth, cheek, or tongue.

Is cystic hygroma a birth defect?

A cystic hygroma — or lymphangioma — is a birth defect that appears as a sac-like structure with a thin wall that most commonly occurs in the head and neck area of an infant. As the baby grows in the womb, it can develop from pieces of material that carries fluid and white blood cells.

What syndrome is associated with cystic hygroma?

Cystic hygroma can be associated with a nuchal lymphangioma or a fetal hydrops. Additionally, it can be associated with Down syndrome, Turner syndrome, or Noonan syndrome.