What is Tolosa Hunt Syndrome?
The Tolosa-Hunt syndrome is a rare syndrome with an estimated annual incidence of one case per million per year [1]. It is characterized by painful ophthalmoplegia (weakness of the eye muscles) and is caused by an idiopathic granulomatous inflammation of the cavernous sinus.
How long does Tolosa Hunt Syndrome last?
The features of THS are caused by inflammation of the cavernous sinus (an area at the base of the brain) but the underlying cause of the inflammation is unknown. Left untreated, symptoms may resolve spontaneously after an average of about eight weeks.
What causes Tolosa Hunt?
Tolosa Hunt syndrome is usually idiopathic and is thought to be from non-specific inflammation in the region of the cavernous sinus and/or superior orbital fissure. However, traumatic injury, tumors, or an aneurysm could be the potential triggers.
Is Tolosa Hunt Syndrome life threatening?
Tolosa-Hunt syndrome is not a fatal disorder; patients experience unilateral onset of acute orbital pain and ophthalmoparesis, and the disorder may threaten sight if untreated inflammation extends beyond the cavernous sinus to affect the optic nerve.
What is Ramsay Hunt syndrome type 2?
Ramsay Hunt syndrome type 2 is caused by reactivation of varicella zoster virus in the geniculate ganglion. Patient often presents with facial nerve paralysis leading to facial droop, dry eyes, mouth and hearing loss.
Is Tolosa Hunt Syndrome autoimmune?
While the exact cause of Tolosa-Hunt syndrome is unknown, one theory is an abnormal autoimmune response linked with an inflammation in a specific area behind the eye (cavernous sinus and superior orbital fissure).
What causes ophthalmoplegia?
What causes ophthalmoplegia? This condition can be congenital (present at birth) or develop later in life. It is generally caused by disruption of the messages that are sent from the brain to the eyes. Internuclear ophthalmoplegia is often caused by multiple sclerosis, trauma, or infarction.
What is the ICD 10 code for Tolosa Hunt Syndrome?
ICD-10 for Tolosa Hunt Syndrome is H49. 40.
How many people have Tolosa Hunt?
Tolosa-Hunt syndrome (THS) is a rare disorder characterized by unilateral ophthalmoplegia and severe unilateral headache. It is a neuro-immunologic disorder considered to be a diagnosis of exclusion. It has an incidence of one per million cases per year.
What kind of doctor treats Ramsay Hunt syndrome?
He or she may refer you to a doctor who specializes in nervous system disorders (neurologist) or to an ear, nose and throat specialist (otolaryngologist).
What is Tolosa Hunt syndrome and what does it mean?
Tolosa Hunt syndrome (THS) is a rare condition characterized by painful ophthalmoplegia (paralysis and/or weakness of the eye muscles).
What kind of headache does Tolosa Hunt have?
Tolosa-Hunt syndrome is a rare disorder characterized by severe periorbital headaches, along with decreased and painful eye movements (ophthalmoplegia).
How long does it take for Tolosa Hunt syndrome to subside?
In most cases, the pain associated with Tolosa-Hunt syndrome subsides with short-term use of steroid drugs. Pain is usually reduced in untreated cases within fifteen to twenty days. With steroid treatment, pain typically briskly subsides within twenty-four to seventy-two hours – and this brisk steroid response aids in the diagnosis.